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KMID : 1103720140700060435
Journal of the Korean Society of Radiology
2014 Volume.70 No. 6 p.435 ~ p.438
CT and MR Imaging Findings of Perianal Dermatofibrosarcoma Protuberans Mimicking Mucinous Adenocarcinoma Arising from Fistula in Ano: A Case Report
Hwang Yun-Sup

Lee Su-Lim
Chang Eun-Deok
Ahn Chang-Hyeok
Ku Young-Mi
Abstract
Dermatofibrosarcoma protuberans (DFSP) is an uncommon soft tissue neoplasm which typically originates in the dermis and spreads into the subcutaneous layer and muscle. We report an extremely rare case of a perianal DFSP mimicking mucinous adenocarcinoma arising from anorectal fistula in a 59-year-old woman. In case of a perianal mass, which is connected by a stalk to the anus and shows heterogeneous enhancement without related regional lymphadenopathy, DFSP should be included in the differential diagnosis.
KEYWORD
Dermatofibrosarcoma Protuberans, Mucinous Adenocarcinoma, Multidetector CT, Magnetic Resonance
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